Synovial chondromatosis is a rare condition in which foci of cartilage develop in the synovial membrane as a result of benign metaplasia of the subsynovial connective tissue. A case report of synovial chondromatosis of the knee joint arising. Synovial chondromatosis, multiple, loose bodies, combined arthroscopy and open surgery introduction synovial chondromatosis is a benign condition characterized by metaplastic changes of the synovial membrane typically affecting large joints 1. Synovial chondromatosis, loose bodies, multiple loose bodies, case reports of knee, hip, shoulder, elbow and ankle joint. P rimary synovial chondromatosis psc is a rare, benign, proliferative disease of hyaline cartilaginous bodies within the synovium of joints. Synovial chondromatosis radiology reference article. Chondrosarcomas of the synovium bertoni 1991 cancer. On both plain films and ct, findings associated with synovial chondromatosis may also include widening. The pain, swelling, and mechanical symptoms of synovial chondromatosis and its generation of loose bodies have historically been treated with surgery. Familial synovial chondromatosis combined with dwarfism. Although described as a benign disease, it can be very destructive and can cause severe osteoarthritis and pain.
Synovial chondromatosis sc has been widely described in great horned owls, mainly affecting the scapulohumeral joints, usually bilaterally, and in most cases at least another joint. The knee is most commonly affected, however it can affect any joint. Locking of the knee caused by localized pigmented villonodular synovitis. Synovial chondromatosis is known by several other names including articular chondrosis and synovial. Synovial chondromatosis is a type of noncancerous tumor that arises in the lining of a joint. Foci on the surface may develop stalks and then detach, resulting in numerous loose bodies within the joint. Synovial chondromatosis is a rare benign condition arising from the synovial membrane of the joints, synovial sheaths or bursa. Oku musculoskeletal tumors aaos 2nd edition 2007, ch 28 pg 265266. Synovial chondromatosis can arise in any joint in the body, but most commonly occurs in the knee. The disease frequently runs a protracted course, often requiring multiple surgical procedures to obtain some control. The synovium has abnormal growth, leading to the production of cartilage bodies which may separate and become loose within the joint. An external file that holds a picture, illustration, etc.
These foci can form free bodies and lead to mechanical arthrosis. Synovial chondromatosis is a rare, benign condition that involves the synovium, the thin layer of tissue that lines joints. Pdf temporomandibular joint synovial chondromatosis. Synovial chondromatosis is a benign cartilaginous metaplasia of the synovium, which may affect any synovial joint. Slideshare uses cookies to improve functionality and performance, and to provide you with relevant advertising.
Extremely rare synovial chondrosarcoma arising from the elbow joint. Osteochondromatosis results when endochondral ossification of the mass occurs, often making it difficult to differentiate from osteochondral fragmentation. It can occur in a number of different joints in the human body, but most commonly occurs at the hip. Primary synovial chondromatosis results from a proliferation of chondrocytes in the synovial membrane leading to the formation of cartilaginous loose bodies. Synovial chondromatosis is an uncommon, benign, process that occurs in large joints, such as the knee 50%, hip, elbow, or shoulder. Synovial chondromatosis in the temporomandibular joint. Synovial chondromatosis usually occurs in large joints, such as the knee or shoulder. Synovial chondromatosis of the temporomandibular joint. Synovial chondromatosis is a rare disorder of the synovium of the joint which causes joint pain and degeneration of the joint if left untreated. Synovial chondromatosis is a disease affecting the synovium, a thin flexible membrane around a joint. A case report of primary synovial chondromatosis with bilateral. Synovial chondromatosis most commonly occurs in adults ages 20 to. We use cookies to make interactions with our website easy and meaningful, to better understand the use of our services, and to tailor advertising.
Synovial chondromatosis presenting as painless soft tissue mass. Synovial chondromatosis of other joints has been reported to occur twice as often in males as in females, with a mean age of onset in the fifth decade. Synovial chondromatosis of the temporomandibular joint is a rare disease, and extraarticular synovial condromatosis of the temporomandibular joint is even rarer. The disease is characteristically monoarticular, most commonly involving the knee. A case of synovial chondromatosis of the temporomandibular joint.
Synovial chondromatosis is a rare condition of unclear etiology in which foci of cartilage develop in the synovial membrane of joints, bursae, or tendon sheaths as a result of metaplasia of the subsynovial connective tissue. Primary synovial chondromatosis sc is a rare proliferative disorder that causes pain, swelling, and restriction of movement to the joints it affects. One possible cause is a change in the level of fibroblast growth receptor factor receptor3, which leads to a possible feedback loop that results in. Hip arthroscopy is an important diagnostic and therapeutic tool in the management of synovial chondromatosis. This process mainly affects synovium and hence most commonly arises from joints and tendons which are lined by synovium. Synovial chondromatosis, also termed synovial osteochondromatosis, is a rare benign disorder characterized by the presence of cartilaginous nodules in the synovium of the joints, tendon sheaths, and bursae. Synovial chondrosarcoma arising in synovial chondromatosis. Knee joint is the most commonly involved joint presenting with pain swelling and restricted movements. Primary synovial chondromatosis is a rare, benign, proliferative disease of hyaline cartilaginous bodies within the synovium of joints.
Synovial osteochondromatosis is a condition characterized by synovial membrane proliferation and metaplasia, with development of multiple cartilaginous or osteocartilaginous nodules within the joint, bursa or tendinous sheath. Synovial chondromatosis an overview sciencedirect topics. Synovial chondromatosis is a rare benign condition which develops in the. The patient with the knee synovial chondromatosis presented as a severly painful edema knee joint, while the symptoms of the other patient is. Radiographic diagnosis of synovial chondromatosis of the. Classification of the disorder was first reported by milgram in 1977. Synovial chondromatosis of the elbow causing a mechanical block to range of motion. The treatment of choice for synovial chondromatosis is a complete surgical excision. A synovial chondromatosis is a rare benign neoplasm on the synovium. Synovial chondromatosis also called synovial osteochondromatosis is a rare, benign noncancerous condition that involves the synovium, which is the thin layer of tissue that lines the joints.
Synovial chondromatosis leads to pain in the affected joint as well as limitation of the range of motion and often locking the cause of synovial chondromatosis is not known. Synovial chondromatosis sc is a chronic process, defined as a reactive cartilaginous proliferation, characterized by formation of cartilaginous nodules, usually loose in the joint space of the synovial membrane. It is a benign, chronic, and progressive condition that does not seem to undergo spontaneous resolution. The synovium in the synovial chonder matosis grows abnormally and produces chondroid. Erosions of bone may be extensive, and the patient can be at risk for developing a pathologic fracture. This article illustrates the imaging characteristics of primary synovial chondromatosis psc using 20 cases referred to a tertiary orthopaedic oncology centre. Synovial chondromatosis of the elbow with asymptomatic ulnar. Synovial chondromatosis is rare joint disorder that has no clear etiology. A rare case of a swollen knee due to disseminated synovial.
Synovial chondromatosis of the elbow with asymptomatic. These nodules can separate and become loose within the joint. Abstract primary synovial chondromatosis is a rare benign neoplastic process which affects. Since the mid 1950s, the technical strategy has included open arthrotomy with removal of loose bodies and synovectomy. Synovial chondromatosis is a disease in which hyaline cartilage can occur in the joint in pedunculated form, within the synovial membrane, or free within the joint. Of 30 patients with synovial chondromatosis, nine had prominent pressure defects at the articular margins of the hip and shoulder. Synovial osteochondromatosis an overview sciencedirect. Hip resurfacing as treatment for synovial chondromatosis.
Removal of osteochondral fragments ocfs from the central and peripheral compartments is crucial for the relief of mechanical symptoms and subsequent joint destruction. During surgery, the surgeon may find multiple freefloating cartilaginous loose bodies in the joint space. It usually occurs aged 30 to 50 years and is extremely rare in children. Neglected synovial osteochondromatosis of the elbow. Secondary synovial chondromatosis is a rare condition characterized by the growth of separated particles from the articular cartilage or osteophytes in joint. Three quarters of patients presented with a large intraarticular soft tissue mass and a suspected clinical and radiological diagnosis of malignancy made in the referring centres. Surgery for synovial chondromatosis 26 cases followed up for 6 years thomas shpitzer, abraham ganel and sandiego engelberg surgery was performed in 31 patients with synovial chondromatosis. In five cases there was evidence of preexisting synovial chondromatosis, and in the remaining three, there was a suggestion of preexisting disease. A disorder of a joint featuring a change of the normal joint lining synovium tissues cellular structure to form cartilage tissue.
Synovial chondroma definition of synovial chondroma by. People usually complain of pain in one joint, which persists for months, or even years, does not ease with exercise, steroid injection or heat treatment, shows nothing on xray, but. Synovial chondromatosis leads to the creation of loose bodies of cartilage alone or in combination. To the best of our knowledge, we report the first known case of an extensive presentation of this intraarticular and extraarticular disease of the knee joint. She links that event with the starting of clicking and light discomfort in right tmj.
Pdf a case report of synovial chondromatosis of the knee. Case report two cases report about the synovial chondromatosis. Few reports exist detailing the natural history of sc, although malignant transformation to synovial chondrosarcoma chs is. Revision arthroscopic surgery for synovial chondromatosis of the hip. A benign neoplasm of welldifferentiated hyaline cartilage originating from the synovial membrane of the joint, the tendinous sheath. Transition to synovial chondrosarcoma rareassociated with multiple recurrences recommended reading. Synovial chondromatosis is a rare condition of metaplastic cartilage development in the synovial membrane of joints. Synovial osteochondromatosis is a benign metaplastic proliferative disorder of the synovium characterised by the formation of multiple cartilaginous nodules in the synovium, many of which detach and become loose bodies. For language access assistance, contact the ncats public information officer. Synovial chondromatosis may also affect bursae and extend into surrounding soft tissues.
Pvns, synovial chondromatosis or lipoma arborescens. Synovial chondromatosis synovial chondrometaplasia. Any information contained in this pdf file is automatically generated from digital material submitted to. Primary synovial chondromatosis typically affects the large joints in the third to fifth decade of life, although. Synovial chondromatosis osteochondromatosis or synovial chondrometaplasia also known as reichel syndrome, is a disorder characterized by loose cartilaginous bodies which may, or may not be calcified or ossified. It most commonly involves large joints, such as the knee, hip, and shoulder, but its presence in smaller joints has also been reported. Primary synovial chondromatosis of the wrist priscilla dagostino, olivier barbier, christine galant, jacques malghem from cliniques universitaires stluc, brussels, belgium. A site in the elbow was first reported in 1918 by henderson, but any joint may be. It can be divided into primary and secondary forms the primary form is uncommon, has unknown causes, and is generally monoarticular.
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